Sclerosing PEComa: A Histologic Surprise

Abstract

PEComa represents a group of mesenchymal tumors consisting of perivascular epithelioid cells. We present a 50-year old female patient with a rare distinctive variant, sclerosing PEComa, characterized by extensive stromal hyalinization and a predilection for the pararenal retroperitoneum.

Key Words: PEComa, Sclerosing PEComa