Neurofibromatosis type 1: a rare cause of parotid swelling in a child

  • Rizwan A. Khan
  • Shagufta Wahab
  • Tariq Mansoor
Keywords: neurofibromatosis type 1, parotid swelling, plexiform neurofibroma

Abstract

Von Recklinghausen disease, also known as neurofibromatosis type 1, is an autosomal dominant disorder that presents as neurocutaneous syndrome. These patients have increased chances of developing other tumors such as plexiform neurofibromas. Plexiform neurofibromas are a proliferation of Schwann cells in the nerve sheath. Affliction of the parotid gland in a young child is a rare presentation of these tumors. We present the management of one such case.

Keywords: neurofibromatosis type 1, parotid swelling, plexiform neurofibroma

Published
2018-02-19
Section
Articles

Journal Identifiers


eISSN: 1687-4137
print ISSN: 1687-4137