Comprehensive dental management in a Hallermann–Streiff syndrome patient with unusual radiographic appearance of teeth

Abstract

Hallermann–Streiff syndrome (HSS) is a genetic disorder characterized by proportionate dwarfism, birdlike facies, hypotrichosis, skin atrophy, dyscephaly, bilateral microphthalmia, congenital cataracts, a narrow, weak, beaked nose, a hypoplastic mandible, and orodental anomalies. Occurrence is sporadic and distinct patterns of inheritance have not been found. This case report describes the dental management of a 3‑year‑old girl patient with HSS, who had unusual radiographic appearance of teeth. Furthermore, dental treatments and a 30‑month follow‑up period of the patient with this rare tooth structure malformation have been presented.

Keywords: Dental anomalies, Hallermann–Streiff syndrome, orofacial characteristics