Pentalogy of Cantrell; complete expression in a nine‑month‑old‑boy

  • Ibrahim Aliyu
  • Mohammad Aminu Mohammad


Pentalogy of Cantrell is a rare congenital malformation whose exact cause is not completely understood; it is characterized by defects in the anterior abdominal and thoracic walls consisting of omphalocoele, diaphragmatic defect, ectopia cordis, intracardiac defects and sternal clefts. The complex has variable clinical expression with complete and incomplete expressions reported. We, therefore, report a case of complete manifestation of the pentad in a 9‑month‑old boy.

Keywords: Cantrell, ectopia cordis, omphalocoele, pentalogy, sternal cleft

Nigerian Medical Journal | Vol. 54 | Issue 3 | May-June | 2013

Author Biographies

Ibrahim Aliyu
Department of Paediatrics, Aminu Kano Teaching Hospital/Bayero University, Kano, Nigeria
Mohammad Aminu Mohammad
Department of Surgery‑Paediatric Surgery Unit, Aminu Kano Teaching Hospital/Bayero University, Kano, Nigeria

Journal Identifiers

eISSN: 2229-774X
print ISSN: 0300-1652