Yellow papules: the iceberg of systemic elastorrhexis

  • Asmae Elhatimi
  • Amal Elbakkal
  • Soraya Iguermia
  • Maryame Meziane
  • Ouafae Mikou
  • Fatima Zahra Mernissi

Abstract

Systemic elastorrhexis is a multisystem genetic disorder characterised by dystrophic mineralization of soft connective tissues in a number of organs, including the skin, the eyes and the arterial blood vessels. Although the eye and skin findings have for years attracted the attention of ophthalmologists and dermatologists, the systemic nature of the disorder has not received sufficient attention among internists and many patients with this disorder have undoubtedly been unrecognized. We reported a case of systemic elastorrhexis redressing the diagnosis of vascular leucoencephalopathy of an unknown aetiology for many years. Key words: Systemic elastorrhexis, pseudoxanthoma elasticum, Gronblad-Strandberg-Touraine.

Pan African Medical Journal 2013; 14: 106

Author Biographies

Asmae Elhatimi
Department of dermatology, HassanII university hospital center, Fez, Morocco
Amal Elbakkal
Department of dermatology, HassanII university hospital center, Fez, Morocco
Soraya Iguermia
Department of dermatology, HassanII university hospital center, Fez, Morocco
Maryame Meziane
Department of dermatology, HassanII university hospital center, Fez, Morocco
Ouafae Mikou
Department of dermatology, HassanII university hospital center, Fez, Morocco
Fatima Zahra Mernissi
Department of dermatology, HassanII university hospital center, Fez, Morocco
Published
2013-05-04
Section
Articles

Journal Identifiers


eISSN: 1937-8688