Cystic hemispheric medulloepithelioma

  • Jacqueline du Toit
  • Tracy Kilborn
  • Llewellyn Padayachy
  • Komala Pillay
  • Marc Hendricks

Abstract

Medulloepithelioma is a rare primitive embryonal tumour of the central nervous system which typically occurs in early childhood. The histopathological appearance has been confused with primitive neuroectodermal tumours (PNETs), but medulloepitheliomas have a more aggressive clinical course. Imaging typically demonstrates a well circumscribed, poorly or non-enhancing solid mass, with cyst formation being infrequent. We report the imaging findings in a case of a cystic hemispheric medulloepithelioma. The importance of considering this diagnosis is discussed in view of the propensity to aggressive recurrence in subtotal resection.

Published
2016-02-03
Section
Articles

Journal Identifiers


eISSN: 2078-6778
print ISSN: 1027-202X