Right posterior diaphragmatic hernia with omphalocele management challenges and benefit of multidisciplinary and multi-inst.pdf

  • J.O Ugwu
  • K.C Etukokwu
  • M P Ufoegbunam
  • C.A Ugwunne
  • N.O Ugwu
Keywords: Neonates, Congenital diaphragmatic hernias, Omphaloceles, Multidisciplinary care

Abstract

Right posterior congenital
diaphragmatic hernias (CDH) with
liver herniations pose a huge
management challenge to the
paediatric surgeons world over. Its
association with anterior abdominal
wall defects portends a poorer
prognosis.
We report a case of a day- old male
referred to our centre with
breathlessness, anterior abdominal
wall defect and persistent poor
oxygen saturation. Clinical and
imaging evaluations aided the
diagnosis of a right posterior
congenital diaphragmatic hernia with
omphalocele and divarication of recti.
Due to dearth of resources, a
multidisciplinary team of paediatric
surgeons, cardiothoracic surgeon,
paediatricians and an intensivist were
assembled and care was undertaken
in two centres to complement in
manpower and facility deficiencies.
This in so many ways mitigated
against likely management
difficulties, morbidities and even
mortality.

CONCLUSION; Right congenital
diaphragmatic hernias (CDH) in a
resource constrained environment
can be successfully managed with
good clinical and multicentre
collaborations.

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Conflict of interest- None declared
Published
2021-11-23
Section
Articles

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print ISSN: 2141-162X