Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association

  • A Batur
  • M Dorum
  • H.A. Yüksekkaya
  • O Koc
Keywords: Behcet´s disease, Budd-Chiari syndrome, renal arterial microaneurysms, aneurysm rupture

Abstract

Behcet’s disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet’s disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior vena cava is rare among the arteries and veins, respectively. When disease affect the veins, it is in the form of thrombosis. Arterial complications include  aneurysms, stenosis and occlusions. Both rupture of arterial aneurysm and occlusion of suprahepatic veins,  causing Budd-Chiari syndrome, are associated with a high mortality rate. Vascular involvement is more common in male patients than in female patients. Men and patients with a younger age of onset present with a more severe prognosis. In this case report, we describe a very rare cause of intrarenal arterial aneurysm’s rupture with  previous Budd-Chiari syndrome due to Behcet’s disease and successful angiographic embolization of actively bleeding aneurysm.
Published
2016-04-13
Section
Articles

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eISSN: 1937-8688