Very large polycystic kidneys presenting with end stage renal failure and massive inguinoscrotal hernia

Abstract

Autosomal Dominant Polycystic Kidney Disease (ADPKD) is the most common inherited cause of renal impairment and End Stage Renal Disease (ESRD).

Apart from cysts in the kidneys and other organs such as the liver, pancreas and other organs, patients also develop abdominal hernia thought to be as a result of increased intra-abdominal pressure and a defect in the formation of collagen matrix.

We report this case of a 51 year old clergyman who presented with massive bilateral polycystic kidneys and a very large inguinoscrotal hernia, the largest we have seen in this practice.

Keywords: Autosomal Dominant Polycystic Kidney Disease (ADPKD), Massive Inguinoscrotal Hernia, Collagen Matrix Disease, Extra cellular matrix