Surgical aspects of ambiguous genitalia associated with congenital adrenal hyperplasia

  • Abdulraouf Y. Lamoshi
  • Bashir El-Gharmooll
Keywords: adrenal hyperplasia, congenital, genitoplasty, intersex

Abstract

Aim The aim of the study was to review the current approach to manage ambiguous genitalia caused by CAH.
Methods This was a retrospective study of 30 patientswith CAH and ambiguous genitalia treated over 10 years. Age at presentation, degree of verilization,  preoperative diagnostic studies, operative technique, blood loss, outcome, and follow-up period were the studied variables.
Results The older 19 patients underwent single-stage feminizing genitoplasty and the younger 11 patients underwent a  multiple-stage procedure. All patients had undergone clitoroplasty, clitoral recession, or resection. Postoperative  complications documented in 23% of the patients included atrophy of the clitoris, flaps complication, and vaginal stenosis. The anatomic and cosmetic outcomes were considered good or satisfactory in 70% and 20% of cases, respectively, and poor in 10% of cases.
Conclusion One-stage or multiple-stage feminizing genitoplasty gives a high percentage of satisfactory cosmetic outcomes. TUM can be implemented to achieve excellent results for complex genitourinary anomalies.

Keywords: adrenal hyperplasia, congenital, genitoplasty, intersex

Published
2018-04-16
Section
Articles

Journal Identifiers


eISSN: 1687-4137
print ISSN: 1687-4137