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Pan African Medical Journal

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Systemic sclerosis in a patient with pityriasis rubra pilaris

F Frikha, M Frigui, H Masmoudi, H Turki, Z Bahloul

Abstract


Pityriasis rubra pilaris (PRP) is a rare, chronic erythematous squamous disorder of unknown etiology. It has been found in association with several autoimmune diseases, including thyroiditis, myositis, myasthenia gravis and vitiligo. Herein we report a case of systemic sclerosis in a patient with classic adult pityriasis rubra pilaris. A 38 year old woman with classic adult type 1 pityriasis rubra pilaris (PRP) developed progressive skin
thickening of the trunk, face, upper and lower extremities after 2 years of PRP treatment with topical emollients and steroids. Clinical examination and immunological findings were consistent with SSc. Co-existence of these two rare conditions is documented for the first time.



http://dx.doi.org/10.4314/pamj.v6i1.69070
AJOL African Journals Online